Severe pancytopenia and splenomegaly associated with felty's syndrome, both fully responsive solely to corticosteroids
نویسندگان
چکیده
In severe cases of pancytopenia with subsequent infections due to long-term untreated Felty's syndrome, the initiation of immunosuppressive treatment with sole prednisone (1 mg/kg iv) should be considered, despite that, the low neutrocytes count would make one physician hesitant. A full resolution of whole blood count within 3 weeks and a 30% reduction in spleens sized was noted.
منابع مشابه
Therapy of Felty's syndrome.
The incidence ofnormocytic hypochromic anaemia in rheumatoid disease is very high (Nilsson, 1948; Empire Rheumatism Council Scientific Advisory Committee, 1950; Jeffrey, 1952); while its aetiology is obscure, its severity appears to fluctuate with exacerbations of joint swellings (Kahlmeter, 1922; Nilsson, 1948). Occasionally the anaemia has the additional feature of a severe leucopenia, and if...
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عنوان ژورنال:
دوره 6 شماره
صفحات -
تاریخ انتشار 2018